ArticleMoulias R, Noble JP, Auriol M, Ernst D, Bouvier AM, Devars Du Mayne JF, Congy F, Loeper J.
Sem Hop. 1979 Mar 8-15;55(9-10):435-41.
The authors report the observation of a 70 years male with Cutis Verticis Gyrata (without hypertrophying osteopathy), Menetrier's hypertrophic gastritis, motrice diarrhea of the endocrine type, flush syndrom, liver angiomatosis and a large sacral water clear cells tumor with horse's tail syndrom. The initial tumor was on the posterior wall of rectum, but was necrosed : bone metastasing chemodectoma, or locally invading carcinoid ? This new complex paraneoplastic disease seems to be associated with APUD tumor.